What is Dandy Walker Malformation?
Dandy Walker Malformation is a congenital (present at birth) malformation of the brain. It involves the cerebellum, which is the lower, hind portion of the brain. Cyst formation and an associated enlargement of the fourth ventricle (cavity within the brain) that frequently results in hydrocephalus (excess fluid in the brain) characterize Dandy Walker Malformation. Hydrocephalus results from the cyst’s interference with the function of draining cerebrospinal fluid from the brain. Dandy Walker Malformation is sometimes seen with other abnormalities such as cleft palate, enlarged kidneys with cysts, spinal cord defects, and other brain defects.